Case Report
Copyright ©The Author(s) 2022. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Clin Cases. Feb 16, 2022; 10(5): 1592-1597
Published online Feb 16, 2022. doi: 10.12998/wjcc.v10.i5.1592
Misdiagnosis of unroofed coronary sinus syndrome as an ostium primum atrial septal defect by echocardiography: A case report
Jin-Ling Chen, Cai-Gui Yu, Dai-Jiao Wang, Hong-Bin Chen
Jin-Ling Chen, Cai-Gui Yu, Dai-Jiao Wang, Department of Echocardiography, Renmin Hospital of Wuhan University, Wuhan 430060, Hubei Province, China
Hong-Bin Chen, Department of Pulmonary and Critical Care Medicine, Renmin Hospital of Wuhan University, Wuhan 430060, Hubei Province, China
Author contributions: Chen JL designed the study and wrote the paper; Chen HB collected the patient’s clinical data; Yu CG and Wang DJ analyzed the data.
Informed consent statement: Informed written consent was obtained from the patient for publication of this report and any accompanying images.
Conflict-of-interest statement: The authors declare that they have no conflicts of interest.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Hong-Bin Chen, PhD, Chief Physician, Department of Pulmonary and Critical Care Medicine, Renmin Hospital of Wuhan University, No. 238 Jiefang Road, Wuchang District, Wuhan 430060, Hubei Province, China. rainman1974@yeah.net
Received: August 10, 2021
Peer-review started: August 10, 2021
First decision: October 16, 2021
Revised: October 24, 2021
Accepted: January 11, 2022
Article in press: January 11, 2022
Published online: February 16, 2022
Processing time: 184 Days and 17.2 Hours
Core Tip

Core Tip: Unroofed coronary sinus syndrome (UCSS) is difficult to diagnose. Transthoracic echocardiography (TTE) of a 37-year-old female revealed ostium primum atrial septal defect (ASD). A second TTE showed type IV UCSS with secundum ASD. Right-heart contrast echocardiography (RHCE) confirmed UCSS and ASD with no persistent left superior vena cava (PLSVC). The patient was misdiagnosed because the defect location was near the endocardial cushions, which was mistaken for a defect of the ostium primum atrial septum. This case highlights the special value of TTE and RHCE for a rare case of type IV UCSS combined with ASD but without PLSVC.