Published online Apr 26, 2021. doi: 10.12998/wjcc.v9.i12.2937
Peer-review started: December 31, 2020
First decision: January 17, 2021
Revised: January 27, 2021
Accepted: February 8, 2021
Article in press: February 8, 2021
Published online: April 26, 2021
Processing time: 104 Days and 13.2 Hours
Budd-Chiari syndrome (BCS) is a rare heterogeneous liver disease characterized by obstruction of the hepatic venous outflow tract. The incidence of BCS is so low that it is difficult to detect in general practice and difficult to include within the scope of routine diagnosis. The clinical manifestations of BCS are not specific; hence, BCS tends to be misdiagnosed.
We report the case of a 33-year-old Chinese woman who presented with progressive distension in the upper abdomen. She was initially misdiagnosed with liver cirrhosis (LC) due to abnormalities on an upper abdominal computed tomography scan. Although she was taking standard anti-cirrhosis therapy, her symptoms did not improve. Magnetic resonance imaging showed caudate lobe hypertrophy; and dilated lumbar and hemiazygos veins. Venography revealed membranous obstruction of the inferior vena cava owing to congenital vascular malformation. A definitive diagnosis of BCS was made. Balloon angioplasty was performed to recanalize the obstructed inferior vena cava and the patient’s symptoms were completely resolved.
BCS lacks specific clinical features and can eventually lead to LC. Clinicians and radiologists must carefully differentiate BCS from LC. Correct diagnosis and timely treatment are vital to the patient's health.
Core Tip: Budd-Chiari syndrome (BCS) is a rare heterogeneous liver disease cha-racterized by obstruction of the hepatic venous outflow tract. We report a case of BCS initially misdiagnosed as liver cirrhosis due to the abnormalities visible on an upper abdominal computed tomography scan. Further examinations were performed to establish a diagnosis. Magnetic resonance imaging revealed a narrowed inferior vena cava. Liver biopsy and pathological analysis showed hepatocyte degeneration, bridging fibrosis, sinusoidal dilatation, and areas of fibrous tissue with substantial hyperplasia, suggesting that BCS was the cause of liver cirrhosis.