Case Report
Copyright ©The Author(s) 2021.
World J Clin Cases. Nov 16, 2021; 9(32): 9960-9969
Published online Nov 16, 2021. doi: 10.12998/wjcc.v9.i32.9960
Table 1 Demographics of two cases

Case 1
Case 2
Birth age (wk)NSVD, 35 + 2NSVD, 41 + 1
Weight at birth (g)21003100
Age of PWS diagnosis5 mon2 yr
Sex MaleMale
Growth hormone therapyOngoing for 4 yrNot applied
Scoliosis surgeryBefore OPPost OP (At respiratory failure)Before OPPost OP (At respiratory failure)
Scoliosis Cobb’s angle (°)66.15482.671.8
Height (cm)134137141143
Weight (kg)53.55779.587
BMI (kg/m2)29.830.440.042.5
Age (yr)12121313
Table 2 Respiratory status before and after noninvasive ventilator apply
Case 1
Case 2
Post OPBefore NIVAfter NIVF/U (5 mo)Post OPBefore NIVAfter NIVF/U (12 mo)
ABG test1
pH7.557.34747.387.4037.3937.37547.37247.384
PaO2 (mmHg)8754.24106.983.363.437.2499.0465.5
PaCO2 (mmHg)4255.2447.736.056.353.4448.9448.9
SaO2 (%)9885.2498.096.391.168.1497.4492.8
Transcutaneous monitoring
SaO2 min (%)NT50490486NTNT744863
SaO2 mean (%)NT89498496NTNT964983
TcCO2 mean (mmHg)NT62.2452.2440.5NTNT42.9441.73
TcCO2 max (mmHg)NT71.6461.1448.1NTNT53.14433
Pulmonary function test
FVC (L)0.9620.68NT0.421.0920.890.840.98
FVC (%)48231NT18472353439
Respiratory muscle strength
MIP (mmHg)NT17NT17452596253
MIP (%)NT19.5NT19.547.4254.956.945.8
MEP (mmHg)NT14NT20982768559
MEP (%)NT13.9NT19.8102.6271.479.852.7
Table 3 Results of polysomnography

Case 1
Case 2
Polysomnography 6 mon after surgery7 mon after surgery
CAI (events/h)00
Obstructive apnea (events/h)101.4
Hypopnea (events/h)8232.5
AHI (events/h)91.233.9
ODI90.231.8
Total arousal index (events/h)49.9
Mean sleep SaO2%74.679.2
Minimal SaO2%5050
Neck circumference (cm)3939