Liver transplantation for late-onset ornithine transcarbamylase deficiency: A case report

Table 1 Laboratory data

Parameter	On admission	After LT	Reference range
Blood ammonia, µmol/L	461.2 ↑	51.2	14-65
Blood lactic acid, mmol/L	4.47 ↑	0.78	0.5-2.2
APTT, s	37.3	24.1	26.1-40.7
PT, s	23.1 ↑	12.6	9.3-12.9
INR	2.030 ↑	1.10	0.72-1.15
Fibrinogen, g/L	1.88	2.36	1.57-3.93
ALT, U/L	73 ↑	44 ↑	0-40
AST, U/L	50 ↑	31	0-40
ALP, U/L	564 ↑	126	40-500
GGT, U/L	15	107 ↑	0-50
TBIL, µmol/L	30.8 ↑	4.0	0.9-17.1
IBIL, µmol/L	25.6 ↑	1.8	2-17
Albumin, g/L	45.5	41.9	35-55
Serum creatinine, µmol/L	63.5	42.3	64-104
Serum uric acid, µmol/L	442.90 ↑	365.6	90-420
Ceruloplasmin	24.4	absent	22-322
Blood amino acids
Glutamine, µmol/L	66.28 ↑	15.83	1.0-55.0
Citrulline, µmol/L	14.7	14.19	5.50-45.00
Arginine, µmol/L	13.57	5.38	1.00-70.00
Urine organic acid
Uracil, mmol/molCr	29.4 ↑	0.0	0.0-8.0
Urinary orotic acid, mmol/molCr	123.3 ↑	0.0	0.0-2.0

↑: Higher than the reference value; LT: Liver transplantation; APTT: Activated partial thromboplastin time; PT: Prothrombin time; INR: International normalized ratio; ALT: Alanine aminotransaminase; AST: Aspartate aminotransferase; ALP: Alkaline phosphatase; GGT: γ-glutamyl transpeptidase; TBIL: Total bilirubin; IBIL: Indirect bilirubin.