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©2014 Baishideng Publishing Group Inc. All rights reserved.
World J Clin Cases. Nov 16, 2014; 2(11): 711-716
Published online Nov 16, 2014. doi: 10.12998/wjcc.v2.i11.711
Published online Nov 16, 2014. doi: 10.12998/wjcc.v2.i11.711
Concomitant achondroplasia and Chiari II malformation: A double-hit at the cervicomedullary junction
Al-Wala Awad, College of Medicine-Phoenix, University of Arizona, Phoenix, AZ 85004, United States
Kyrieckos A Aleck, Division of Genetics and Metabolism, Phoenix Children’s Hospital, Phoenix, AZ 85016, United States
Ratan D Bhardwaj, Division of Neurological Surgery, Barrow Neurological Institute at Phoenix Children’s Hospital, Phoenix, AZ 85016, United States
Author contributions: All the authors solely contributed to this paper.
Correspondence to: Al-Wala Awad, BS, College of Medicine-Phoenix, University of Arizona, 550 E. Van Buren St, Phoenix, AZ 85004, United States. wala.awad@gmail.com
Telephone: +1-480-2921480
Received: April 26, 2014
Revised: July 28, 2014
Accepted: September 4, 2014
Published online: November 16, 2014
Processing time: 198 Days and 5.5 Hours
Revised: July 28, 2014
Accepted: September 4, 2014
Published online: November 16, 2014
Processing time: 198 Days and 5.5 Hours
Core Tip
Core tip: Achondroplasia and Chiari II malformations can induce similar anatomical changes at the cervicomedullary junction which increase the risk of acute hydrocephalus. Chiari decompression may not always be necessary, however, diligent and acute follow-up is important to monitor for signs of impeding hydrocephalus. If cerebral spinal fluid diversion is required, remember that shunt failure is common in the pediatric age group and also requires close follow-up.