Published online Jun 16, 2021. doi: 10.12998/wjcc.v9.i17.4423
Peer-review started: February 9, 2021
First decision: February 28, 2021
Revised: March 9, 2021
Accepted: March 25, 2021
Article in press: March 25, 2021
Published online: June 16, 2021
Processing time: 105 Days and 17.9 Hours
Paraneoplastic cerebellar degeneration (PCD), which is rare in clinical practice, is closely related to autoimmunity. Cases positive for anti-Yo antibodies (anti-Purkinje cytoplasmic antibody 1) are the main subtype of PCD. PCD is subacute cerebellar degeneration, and while it progresses over weeks to months, its resultant deficits last much longer. Cancer patients with anti-Yo antibody-positive PCD are very rare. Most of them are breast cancer or ovarian cancer patients but also occasionally lung cancer patients.
A 61-year-old woman presented with sudden vertigo, nausea, and vomiting for approximately 10 d. The patient's neurological examination showed torsion with downbeat nystagmus and ataxia of the right limb and trunk. Laboratory examination found that the patient's cerebrospinal fluid and serum were anti-Yo antibody-positive, positron emission tomography computed tomography showed an increased metabolic rate in the retroperitoneal lymph nodes, and the pathology of lymph node punctures in the retroperitoneum and neck suggested adenocarcinoma of the pancreaticobiliary duct, which strengthens the hypothesis of paraneoplastic origin. Intravenous immunoglobulin (IVIg) 0.4 g/kg/d for 5 d and methylprednisolone 160 mg for 3 d were initiated, which was reduced to 80 mg for 3 d and then to 40 mg for 7 d. After treatment with IVIg and a steroid, the patient's vertigo and ataxia alleviated.
The patient's vertigo and ataxia alleviated after treatment, suggesting that early immunotherapeutic intervention may have certain value in stopping neurological loss.
Core Tip: We report for the first time a female patient with anti-Yo antibody-positive paraneoplastic cerebellar degeneration (PCD), who was later diagnosed with possible cholangiocarcinoma. She presented with sudden vertigo, nausea, and vomiting for approximately 10 d. The brain magnetic resonance imaging examination showed no obvious abnormalities. Finally, the pathology of lymph node punctures in the retroperitoneum and neck suggested adenocarcinoma of the pancreaticobiliary duct. The patient's symptoms alleviated with intravenous immunoglobulin and steroid treatment. This case highlighted that early immunotherapeutic intervention may stop and reverse neurological loss in PCD.