Wang L, Feng Y, Jiang LY. Anesthetic management of bilateral pheochromocytoma resection in Von Hippel-Lindau syndrome: A case report. World J Clin Cases 2021; 9(15): 3711-3715 [PMID: 34046474 DOI: 10.12998/wjcc.v9.i15.3711]
Corresponding Author of This Article
Lu-Yang Jiang, MD, Associate Professor, Department of Anesthesiology, Peking University People’s Hospital, No. 11 Xizhimen South Street, Xicheng District, Beijing 100044, China. jiangluyang@pkuph.edu.cn
Research Domain of This Article
Anesthesiology
Article-Type of This Article
Case Report
Open-Access Policy of This Article
This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
World J Clin Cases. May 26, 2021; 9(15): 3711-3715 Published online May 26, 2021. doi: 10.12998/wjcc.v9.i15.3711
Anesthetic management of bilateral pheochromocytoma resection in Von Hippel-Lindau syndrome: A case report
Lu Wang, Yi Feng, Lu-Yang Jiang
Lu Wang, Yi Feng, Lu-Yang Jiang, Department of Anesthesiology, Peking University People’s Hospital, Beijing 100044, China
Author contributions: Wang L reviewed the records and contributed to manuscript drafting; Feng Y and Jiang LY, the patient’s anesthesiologists, reviewed the literature and contributed to manuscript revision; all authors issued final approval for the version to be submitted.
Informed consent statement: Informed written consent was obtained from the patient for publication of this report and any accompanying images.
Conflict-of-interest statement: The authors declare that they have no conflict of interest.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Lu-Yang Jiang, MD, Associate Professor, Department of Anesthesiology, Peking University People’s Hospital, No. 11 Xizhimen South Street, Xicheng District, Beijing 100044, China. jiangluyang@pkuph.edu.cn
Received: December 27, 2020 Peer-review started: December 28, 2020 First decision: January 24, 2021 Revised: February 1, 2021 Accepted: March 18, 2021 Article in press: March 18, 2021 Published online: May 26, 2021 Processing time: 135 Days and 4.6 Hours
Abstract
BACKGROUND
Von Hippel-Lindau disease (also known as VHL syndrome), is an autosomal dominant inherited disease. We describe a sporadic case of VHL syndrome where bilateral pheochromocytomas were unexpectedly identified. The patient underwent selective laparoscopic resections of the pheochromocytomas, and the anesthetic management during surgery was complex and challenging.
CASE SUMMARY
A 22-year-old man presented to our hospital to seek medical advice for infertility without any other complaints. The results of computed tomography and catecholamine levels in blood and urine demonstrated adrenal gland masses which were diagnosed as pheochromocytomas. Further examination confirmed that the patient also had VHL syndrome. After thorough preparation, the patient underwent selective laparoscopic resection of the pheochromocytomas and was discharged 10 d after surgery. We describe the process of perioperative anesthesia management in this patient undergoing pheochromocytoma resection.
CONCLUSION
This case summaries specific clinical traits and considerations in perioperative anesthesia management for VHL syndrome patients undergoing bilateral pheochromocytoma resection.
Core Tip: Von Hippel-Lindau (VHL) syndrome is a rare autosomal dominant inherited disease, and anesthesia for patients with VHL syndrome undergoing bilateral pheochromocytoma resection involves some unique considerations. This case highlights the process of anesthesia, including preparation, monitoring and perioperative management.
