Published online Sep 26, 2020. doi: 10.12998/wjcc.v8.i18.4169
Peer-review started: May 29, 2020
First decision: June 13, 2020
Revised: June 23, 2020
Accepted: August 22, 2020
Article in press: August 22, 2020
Published online: September 26, 2020
Processing time: 115 Days and 12.4 Hours
Insulinomas are the most common type of functioning endocrine neoplasms of the pancreas presenting hypoglycemic symptoms. Patients characteristically develop symptoms while fasting, but some patients have reported symptoms only in the postprandial state. Repeated and prolonged hypoglycemic episodes can reduce the awareness of adrenergic symptoms, and patients may have amnesia, which delays diagnosis.
We describe a case of a 24-year-old underweight patient who showed hypoglycemic symptoms for almost 6 years. Although patients with insulinoma characteristically develop symptoms while fasting, this young man had hypoglycemic symptoms up to one hour postprandially, especially after high-sugar meals and after physical activity. The fasting tests and imaging methods performed at local hospitals were evaluated as negative for abnormal results. However, brown adipose tissue exhibited increased metabolic activity, and some muscle groups had histological changes as indicated by positron emission tomography with 2-deoxy-2-[fluorine-18]fluoro-D-glucose integrated with computed tomography. Glycogen deficiency was also histologically confirmed. The patient’s symptoms progressed over the years and occurred more frequently, i.e., several times a month, and the patient had reduced awareness of adrenergic symptoms. The follow-up fasting test was positive, and the imaging results showed a tumor in the head of the pancreas. The patient underwent laparotomy with enucleation of the insulinoma.
Weight gain and fasting hypoglycemia are not necessarily characteristics of insulinoma. In prolonged cases, adrenergic symptoms can be suppressed.
Core Tip: Postprandial hypoglycemia and hypoglycemia following physical exercise associated with unconsciousness/amnesia and a low body weight were the clinical features of insulinoma in a 24-year-old man for over 6 years. The consequences of the chronic counterregulatory adrenergic response were also indirectly indicated by the increased metabolic activity of brown adipose tissue and decrease in muscle glycogen content, although the fasting test and other imaging results were initially evaluated as normal. Therefore, if insulinoma is clinically suspected, the fasting test should be repeated. The patient was underweight with a very small amount of visceral fat, which increases the risk of perioperative complications.