Liu Z, Xu YH, Ge CL, Long J, Du RX, Guo KJ. Huge peripheral primitive neuroectodermal tumor of the small bowel mesentery at nonage: A case report and review of the literature. World J Clinical Cases 2016; 4(9): 306-309 [PMID: 27672649 DOI: 10.12998/wjcc.v4.i9.306]
Corresponding Author of This Article
Zhe Liu, MD, Department of Pancreatic Surgery, the First Hospital of China Medical University, Heping District, Nanjing Road No. 155, Shenyang 110001, Liaoning Province, China. liuzhe4321@126.com
Research Domain of This Article
Gastroenterology & Hepatology
Article-Type of This Article
Case Report
Open-Access Policy of This Article
This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
World J Clinical Cases. Sep 16, 2016; 4(9): 306-309 Published online Sep 16, 2016. doi: 10.12998/wjcc.v4.i9.306
Huge peripheral primitive neuroectodermal tumor of the small bowel mesentery at nonage: A case report and review of the literature
Zhe Liu, Yuan-Hong Xu, Chun-Lin Ge, Jin Long, Rui-Xia Du, Ke-Jian Guo
Zhe Liu, Yuan-Hong Xu, Chun-Lin Ge, Jin Long, Ke-Jian Guo, Department of Pancreatic Surgery, the First Hospital of China Medical University, Shenyang 110001, Liaoning Province, China
Rui-Xia Du, Department of Otorhinolaryngology, Fengtian Hospital, Shenyang Medical University, Shenyang 110001, Liaoning Province, China
Author contributions: All authors contributed to the acquisition of data, writing and revision of the manuscript.
Institutional review board statement: This case report is retrospective and was not antecedently reviewed by the Local Ethics committee of China Medical University.
Informed consent statement: The patient involved in this study gave his written informed consent authorizing use and disclosure of his protected health information.
Conflict-of-interest statement: The authors declared that they have no conflicts of interest to this work.
Open-Access: This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
Correspondence to: Zhe Liu, MD, Department of Pancreatic Surgery, the First Hospital of China Medical University, Heping District, Nanjing Road No. 155, Shenyang 110001, Liaoning Province, China. liuzhe4321@126.com
Telephone: +86-24-83283330 Fax: +86-24-83283350
Received: January 25, 2016 Peer-review started: January 26, 2016 First decision: May 17, 2016 Revised: May 25, 2016 Accepted: June 14, 2016 Article in press: June 16, 2016 Published online: September 16, 2016 Processing time: 226 Days and 0.5 Hours
Abstract
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor (E-EWS/pPNET) is a rare aggressive malignant small round cell tumor. In this report, we present the case of a 15-year-old boy who suffered from acute abdominal pain accompanied by hematemesis and melena, and was eventually diagnosed with E-EWS/pPNET. To date, there have been only five reported cases of E-EWS/pPNET of the small bowel including the patient in this report. To the best of our knowledge, this is the first documentation of a pPNET of the small bowel mesentery at nonage. All these have made this report rare and significant.
Core tip: Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumors (E-EWS/pPNETs) are rare aggressive malignant small round cell tumors that are derived from the outer central and autonomic nervous systems. To date, there have been only five reported cases of E-EWS/pPNET of the small bowel including the patient presented in this report. The patient presented in this report is the youngest and had the worst prognosis.