Case Report
Copyright ©The Author(s) 2024. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Clin Cases. Jun 16, 2024; 12(17): 3183-3187
Published online Jun 16, 2024. doi: 10.12998/wjcc.v12.i17.3183
Regional anesthesia in a patient with primary ciliary dyskinesia: A case report
Hyung Joon Park, Ye Hwan Kim, Young Joon Yoon, Sang Yun Cho
Hyung Joon Park, Ye Hwan Kim, Young Joon Yoon, Sang Yun Cho, Department of Anesthe-siology and Pain Medicine, Hanyang University Guri Hospital, Guri-si 471-701, Gyeonggi-do, South Korea
Author contributions: Park HJ, Kim YH, Yoon YJ and Cho SY wrote and revised the manuscript; and all authors have read and approve the final manuscript.
Informed consent statement: This report was prepared with the written consent of the patient.
Conflict-of-interest statement: All the authors report no relevant conflicts of interest for this article.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript was prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/licenses/by-nc/4.0/
Corresponding author: Sang Yun Cho, MD, PhD, Department of Anesthesiology and Pain Medicine, Hanyang University Guri Hospital, 249-1, Gyomun-dong, Guri-si 471-701, Gyeonggi-do, South Korea. chosy@hanyang.ac.kr
Received: January 30, 2024
Revised: April 9, 2024
Accepted: April 22, 2024
Published online: June 16, 2024
Processing time: 126 Days and 11.6 Hours
Abstract
BACKGROUND

Primary ciliary dyskinesia (PCD) is an inherited autosomal-recessive disorder of impaired mucociliary clearance characterized by chronic respiratory diseases, otolaryngological diseases, central nervous system abnormalities, reproductive system abnormalities, and cardiac function abnormalities. General anesthesia in these patients is associated with a higher incidence of respiratory complications than in patients without the disease.

CASE SUMMARY

A 16-year-old male patient was referred to the emergency room complaining of right ankle pain due to distal tibiofibular fracture. Three years prior, he had been diagnosed with PCD. At that time, he had experienced several episodes of pneumonia, sinusitis, and chronic middle ear infections, for which he underwent surgical interventions. At the current admission, he presented with cough and sputum but no other respiratory symptoms. A chest computed tomography scan revealed centrilobular ground-glass opacities in both lower lobes and a calcified nodule in the left lower lobe. For the surgical procedure and postoperative pain management, combined spinal-epidural anesthesia was employed. The patient’s postoperative pain score was measured by the numerical rating scale (NRS). On the day of surgery, his NRS was 5 points. By the second postoperative day, the NRS score had decreased to 2–3 points. The epidural catheter was removed on the fourth day following the operation. The patient was subsequently discharged no respiratory complications.

CONCLUSION

We performed combined spinal-epidural anesthesia in a patient with PCD. The patient experienced no additional respiratory complications and was discharged with a low NRS score for pain.

Keywords: Primary ciliary dyskinesia, Combined spinal-epidural anesthesia, Patient controlled epidural analgesia, Lower limb operation, Case report.

Core Tip: Primary ciliary dyskinesia (PCD) is an inherited autosomal-recessive disorder of impaired mucociliary clearance. General anesthesia in these patients is associated with a higher incidence of respiratory complications. We performed combined spinal-epidural anesthesia in a patient with PCD. The patient experienced no additional respiratory complications and was discharged with a low numerical rating scale score for pain.