Published online Nov 16, 2023. doi: 10.12998/wjcc.v11.i32.7881
Peer-review started: September 4, 2023
First decision: September 28, 2023
Revised: October 11, 2023
Accepted: November 9, 2023
Article in press: November 9, 2023
Published online: November 16, 2023
Processing time: 73 Days and 2.5 Hours
Median arcuate ligament syndrome (MALS) is a rare disease caused by compre
A 55-year-old woman was admitted due to abdominal pain, nausea and vomiting. On admission, the patient presented with epigastric pain that worsened after eating, without signs of peritoneal irritation. Computed tomography angiography of the upper abdomen showed compression of the proximal segment of the abdominal trunk, local luminal stenosis with angular “fishhook” changes, which changed significantly during forceful inspiration and expiration; gallbladder stones; and multiple cysts in the liver. Abdominal duplex ultrasonography showed that peak systolic velocity was 352 cm/s. After diagnosis of MALS was confirmed, an arch ligament release procedure was performed. MALS has no specific symptoms and can be misdiagnosed as other abdominal diseases. Awareness of MALS should be improved to avoid misdiagnosis. The commonly used treatment option is MAL release and resection of the peripheral ganglion of the celiac trunk artery.
The diagnosis and treatment of MALS must be individualized, and MAL release is effective and provides immediate symptomatic relief.
Core Tip: Median arcuate ligament syndrome (MALS) is a rare disorder caused by compression of the median arcuate ligament against the celiac trunk. Patients with MALS often present with chronic postprandial abdominal pain, nausea, vomiting, diarrhea, and unexplained weight loss. Imaging examination is the preferred screening method. MALS is confused with many common diseases, and definitive diagnosis requires exclusion of other causes of abdominal pain. In this case, combination of gallbladder stones and chronic cholecystitis made it easy to miss diagnosis of MALS. Clinicians should be more aware of MALS. Surgery can provide immediate symptomatic relief and can be an effective treatment for MALS.