Choi S, Park SH, Kim JS, Chang J. Congenital stapes suprastructure fixation presenting with fluctuating auditory symptoms: A case report. World J Clin Cases 2023; 11(1): 249-254 [PMID: 36687180 DOI: 10.12998/wjcc.v11.i1.249]
Corresponding Author of This Article
Jiwon Chang, MD, PhD, Associate Professor, Department of Otolaryngology-Head and Neck Surgery, Kangnam Sacred Heart Hospital, Hallym University College of Medicine, 1 Singil-ro, Yeongdeungpo-gu, Seoul 07441, South Korea. brune77@naver.com
Research Domain of This Article
Otorhinolaryngology
Article-Type of This Article
Case Report
Open-Access Policy of This Article
This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
World J Clin Cases. Jan 6, 2023; 11(1): 249-254 Published online Jan 6, 2023. doi: 10.12998/wjcc.v11.i1.249
Congenital stapes suprastructure fixation presenting with fluctuating auditory symptoms: A case report
Sun Choi, Seok Hyun Park, Ji Su Kim, Jiwon Chang
Sun Choi, Seok Hyun Park, Ji Su Kim, Jiwon Chang, Department of Otolaryngology-Head and Neck Surgery, Kangnam Sacred Heart Hospital, Hallym University College of Medicine, Seoul 07441, South Korea
Author contributions: Choi S and Park SH contributed to manuscript writing and editing and data collection; Kim JS contributed to data analysis; Chang J contributed to conceptualization and supervision; and all authors have read and approved the final manuscript.
Informed consent statement: Written informed consent was obtained from the patient for publication of this case report and any accompanying images.
Conflict-of-interest statement: All the authors report no relevant conflicts of interest for this article.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript has been prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Jiwon Chang, MD, PhD, Associate Professor, Department of Otolaryngology-Head and Neck Surgery, Kangnam Sacred Heart Hospital, Hallym University College of Medicine, 1 Singil-ro, Yeongdeungpo-gu, Seoul 07441, South Korea. brune77@naver.com
Received: November 2, 2022 Peer-review started: November 2, 2022 First decision: November 22, 2022 Revised: November 30, 2022 Accepted: December 21, 2022 Article in press: December 21, 2022 Published online: January 6, 2023 Processing time: 63 Days and 14.4 Hours
Abstract
BACKGROUND
Stapes ankylosis is a rare cause of conductive hearing loss, and stapes suprastructure fixation is extremely rare with fewer than 30 reported cases. Patients usually visit the clinic with non-progressive conductive hearing loss that typically began in the early years of life.
CASE SUMMARY
Herein, we report a case of a 37-year-old female with an isolated stapedial suprastructure fixation. The patient presented with unusual fluctuating auditory symptoms of tinnitus, ear fullness and mixed hearing loss. Pre-operative temporal bone computed tomography findings and operative findings revealed an isolated stapedial suprastructure fixation with monopod stapes caused by elongated pyramidal eminence. The hearing threshold recovered completely, and fluctuating auditory symptoms disappeared after the surgery.
CONCLUSION
This is the first report of stapedial suprastructure fixation with fluctuating auditory symptoms. Successful results are expected with surgical treatment.
Core Tip: Stapes ankylosis is rare disease presenting with non-progressive conductive hearing loss that usually begins in the early years of life. However, as noted in our case, the patient might present with fluctuating auditory symptoms, such as tinnitus, ear fullness and alternating mixed hearing loss. When a persistent air bone gap is noted in audiometry, the possibility of middle ear anomaly should be suspected and successful results can be obtained with surgical treatment.
