Case Report
Copyright ©The Author(s) 2023. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Clin Cases. Jan 6, 2023; 11(1): 249-254
Published online Jan 6, 2023. doi: 10.12998/wjcc.v11.i1.249
Congenital stapes suprastructure fixation presenting with fluctuating auditory symptoms: A case report
Sun Choi, Seok Hyun Park, Ji Su Kim, Jiwon Chang
Sun Choi, Seok Hyun Park, Ji Su Kim, Jiwon Chang, Department of Otolaryngology-Head and Neck Surgery, Kangnam Sacred Heart Hospital, Hallym University College of Medicine, Seoul 07441, South Korea
Author contributions: Choi S and Park SH contributed to manuscript writing and editing and data collection; Kim JS contributed to data analysis; Chang J contributed to conceptualization and supervision; and all authors have read and approved the final manuscript.
Informed consent statement: Written informed consent was obtained from the patient for publication of this case report and any accompanying images.
Conflict-of-interest statement: All the authors report no relevant conflicts of interest for this article.
CARE Checklist (2016) statement: The authors have read the CARE Checklist (2016), and the manuscript has been prepared and revised according to the CARE Checklist (2016).
Open-Access: This article is an open-access article that was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution NonCommercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: https://creativecommons.org/Licenses/by-nc/4.0/
Corresponding author: Jiwon Chang, MD, PhD, Associate Professor, Department of Otolaryngology-Head and Neck Surgery, Kangnam Sacred Heart Hospital, Hallym University College of Medicine, 1 Singil-ro, Yeongdeungpo-gu, Seoul 07441, South Korea. brune77@naver.com
Received: November 2, 2022
Peer-review started: November 2, 2022
First decision: November 22, 2022
Revised: November 30, 2022
Accepted: December 21, 2022
Article in press: December 21, 2022
Published online: January 6, 2023
Processing time: 63 Days and 14.4 Hours
Abstract
BACKGROUND

Stapes ankylosis is a rare cause of conductive hearing loss, and stapes suprastructure fixation is extremely rare with fewer than 30 reported cases. Patients usually visit the clinic with non-progressive conductive hearing loss that typically began in the early years of life.

CASE SUMMARY

Herein, we report a case of a 37-year-old female with an isolated stapedial suprastructure fixation. The patient presented with unusual fluctuating auditory symptoms of tinnitus, ear fullness and mixed hearing loss. Pre-operative temporal bone computed tomography findings and operative findings revealed an isolated stapedial suprastructure fixation with monopod stapes caused by elongated pyramidal eminence. The hearing threshold recovered completely, and fluctuating auditory symptoms disappeared after the surgery.

CONCLUSION

This is the first report of stapedial suprastructure fixation with fluctuating auditory symptoms. Successful results are expected with surgical treatment.

Keywords: Isolated stapes ankylosis; Stapes suprastructure fixation; Elongated pyramidal eminence; Stapes monopod; Fluctuating auditory symptoms; Exploratory tympanotomy; Case report

Core Tip: Stapes ankylosis is rare disease presenting with non-progressive conductive hearing loss that usually begins in the early years of life. However, as noted in our case, the patient might present with fluctuating auditory symptoms, such as tinnitus, ear fullness and alternating mixed hearing loss. When a persistent air bone gap is noted in audiometry, the possibility of middle ear anomaly should be suspected and successful results can be obtained with surgical treatment.