Published online Jun 26, 2022. doi: 10.12998/wjcc.v10.i18.6289
Peer-review started: December 26, 2021
First decision: March 7, 2022
Revised: March 20, 2022
Accepted: April 24, 2022
Article in press: April 24, 2022
Published online: June 26, 2022
Left-dominant arrhythmogenic cardiomyopathy (LDAC) is a relatively rare disease characterized by poor prognosis that exacerbates the incidence of sudden cardiac death and ventricular arrhythmias. Clinically, LDAC is constantly overlooked or misdiagnosed as myocardial infarction, myocarditis, and dilated cardiomyopathy, owing to atypical and nonspecific clinical manifestations at an early stage.
A 57-year-old woman was diagnosed with sinus bradycardia and chronic bifascicular block during a health check. She occasionally experienced mild chest pain and paroxysmal palpitation during activity in the past 2 years. Comprehensive auxiliary examinations, including electrocardiogram, echocardiography, coronary computerized tomography angiography, and magnetic resonance imaging, revealed that she had LDAC instead of congenital ventricular diver
Based on this case, clinicians need to be aware of LDAC in patients with localized left ventricular lesions and multiple electrocardiographic abnormalities. Mul
Core Tip: Left-dominant arrhythmogenic cardiomyopathy is a relatively rare disease, characterized by poor prognosis. We present a case with a dilated left ventricle that manifested with reduced ejection fraction, multiple outpouchings, left chest leads low voltage, and fragmented QRS. Multimodality cardiovascular imaging diagnosed the patient with left-dominant arrhythmogenic cardiomyopathy instead of congenital ventricular diverticulum. This case alerts clinicians to be aware of left-dominant arrhythmogenic cardiomyopathy in patients with localized left ventricular lesions and multiple electrocardiographic abnormalities.