Published online Jul 16, 2013. doi: 10.12998/wjcc.v1.i4.146
Revised: May 14, 2013
Accepted: June 1, 2013
Published online: July 16, 2013
Ruptured sinus of Valsalva is very uncommon, and is < 1% of all congenital defects. The incidence ranges from 0.1%-3.5%. There is a male to female predominance of 4:1, with the highest incidence in the Asian population. Higher incidence is also seen in patients with Marfan’s syndrome and Ehlers Danlos syndrome. There is a higher association of ruptured sinus of Valsalva with ventricular septal defect (VSD), aortic stenosis, and bicuspid valve defect. While most patients with VSD often have rupture of their right coronary sinus of Valsalva into the right ventricle due to poor structural integrity, we present a rare case of a patient with VSD who had rupture of his noncoronary sinus of Valsalva into the right atrium.
Core tip: It is important to understand that aneurysms and or rupture of the coronary sinus of Valsalva can occur from any sinus and into any chamber, which will affect management and treatment.