Pasman EA, Heifert TA, Nylund CM. Esophageal squamous papillomas with focal dermal hypoplasia and eosinophilic esophagitis. World J Gastroenterol 2017; 23(12): 2246-2250 [PMID: 28405153 DOI: 10.3748/wjg.v23.i12.2246]
Corresponding Author of This Article
Cade M Nylund, MD, Program Director, Pediatric Gastroenterology, Hepatology, and Nutrition Fellowship Program, National Capital Consortium, 8901 Wisconsin Ave, Bethesda, MD 20889, United States. cade.nylund@usuhs.edu
Research Domain of This Article
Gastroenterology & Hepatology
Article-Type of This Article
Case Report
Open-Access Policy of This Article
This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
World J Gastroenterol. Mar 28, 2017; 23(12): 2246-2250 Published online Mar 28, 2017. doi: 10.3748/wjg.v23.i12.2246
Esophageal squamous papillomas with focal dermal hypoplasia and eosinophilic esophagitis
Eric A Pasman, Theresa A Heifert, Cade M Nylund
Eric A Pasman, Pediatric Residency Program, National Capital Consortium, Bethesda, MD 20889, United States
Theresa A Heifert, Cade M Nylund, Pediatric Gastroenterology, Hepatology and Nutrition Fellowship Program, National Capital Consortium, Bethesda, MD 20889, United States
Cade M Nylund, Department of Pediatrics, F. Edward Hebert School of Medicine, Uniformed Services University, Bethesda, MD 20814, United States
Author contributions: Pasman EA drafted the initial manuscript; Pasman EA, Heifert TA and Nylund CA were involved in the clinical care of the case and edited the manuscript.
Institutional review board statement: The study was approved by the Walter Reed National Military Medical Center at Bethesda Institutional Review Board.
Informed consent statement: The legal guardian of the subject of this case gave verbal and written informed consent for this study.
Conflict-of-interest statement: The authors have no disclosures. This case report discusses use of the ERBE VIO APC system (ERBE USA Inc, Marietta, Georgia) and the proprietary PRECISE setting. The authors have no affiliation with ERBE.
Open-Access: This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
Correspondence to: Cade M Nylund, MD, Program Director, Pediatric Gastroenterology, Hepatology, and Nutrition Fellowship Program, National Capital Consortium, 8901 Wisconsin Ave, Bethesda, MD 20889, United States. cade.nylund@usuhs.edu
Telephone: +1-301-2951446
Received: January 11, 2017 Peer-review started: January 12, 2017 First decision: February 9, 2017 Revised: February 24, 2017 Accepted: March 4, 2017 Article in press: March 4, 2017 Published online: March 28, 2017 Processing time: 76 Days and 20.7 Hours
Abstract
Focal dermal hypoplasia (FDH) is a rare disorder of the mesodermal and ectodermal tissues. Here we present an eight-year-old female known to have FDH who presents with poor weight gain and dysphagia. She was diagnosed with multiple esophageal papillomas and eosinophilic esophagitis. She was successfully treated with argon plasma coagulation and ingested fluticasone propionate, which has not been described previously in a child.
Core tip: Focal dermal hypoplasia (FDH) is a rare connective tissue disorder associated with squamous papillomas of the esophagus in older individuals. This case discusses an 8-year-old female with FDH who presented with dysphagia. She was found to have esophageal papillomas and eosinophilic esophagitis. Treatment of eosinophilic esophagitis is highlighted. Argon plasma coagulation has been shown to be safe for use in the small diameter of the esophagus of children but not specifically for destruction of esophageal papillomas. A successful approach to debulking esophageal papillomas in a child using argon plasma coagulation is described in this case.
