Unilateral pleuroparenchymal fibroelastosis as a rare form of idiopathic interstitial pneumonia: A case report

Figure 1 Chest X-ray showed subpleural and irregular shaped increased opacity in right upper lung zone. Sequential changes during 6 mo showed increased opacity in right upper lung zone. A: Initial visit of diagnosis; B: After 3 mo; C: After 6 mo.

Figure 2 High-resolution computed tomography revealed subpleural thickening and consolidation with traction bronchiectasis in only right upper lung field. Follow-up high-resolution computed tomography showed increased alveolar collapse with consolidation and volume loss compared to 6 mo ago. A: Right upper lobe at initial visit; B: Carina level at initial visit; C: Right lower lobe at initial visit; D: Right upper lobe after 6 mo; E: Carina level after 6 mo; F: Right lower lobe after 6 mo.

Figure 3 Transbronchial lung biopsy specimen in right upper lobe. A: On higher magnification view, hematoxylin and eosin-stained images revealed dense fragmentation and dilated alveolar space surrounding alveolar with elastosis; B: Elastic van Gieson stain demonstrated septal elastosis (orange arrows) with intra-alveolar collagenosis.