Rapid improvement in postpartum pulmonary hypertension associated with hereditary hemorrhagic telangiectasia: A case report and review of literature

Figure 1 Identification of a heterozygous variant of ACVRL1 in the patient.

Figure 2 The patient’s clinical manifestations at admission. A and B: The patient’s imaging presentation on admission, bilateral pulmonary arteriovenous malformations shown by the orange arrows; C and D: Telangiectases (black arrows) are observed in both distant and closer views of the palm of the patient’s hands; E and F: Telangiectases (black arrows) are observed in both distant and closer views of back of the patient’s hands.

Figure 3 Changes in this case at the time of treatment. A: Changes in pulmonary artery systolic pressure ratio of this case under treatments; B: Changes in N-terminus pro-brain natriuretic peptide ratio of this case under treatments; C: Changes in PaO₂ or PaCO₂ ratio of this case under treatments; D: Changes in PaO₂/FiO₂ ratio of this case under treatments. PASP: Pulmonary artery systolic pressure; NT-proBNP: N-terminus pro-brain natriuretic peptide; P/F: PaO₂/FiO₂; NO: Nitric oxide.