Review
Copyright ©2012 Baishideng. All rights reserved.
World J Nephrol. Apr 6, 2012; 1(2): 54-62
Published online Apr 6, 2012. doi: 10.5527/wjn.v1.i2.54
Bone disease in pediatric idiopathic hypercalciuria
Maria Goretti Moreira Guimarães Penido, Marcelo de Sousa Tavares
Maria Goretti Moreira Guimarães Penido, Marcelo de Sousa Tavares, Department of Pediatrics, Pediatric Nephrology Unit, School of Medicine, Federal University of Minas Gerais, Belo Horizonte, Belo Horizonte, CEP 30130100, Minas Gerais, Brazil
Author contributions: Moreira Guimarães Penido MG and de Sousa Tavares M contributed equally to the conception and design of the study, the acquisition, analysis and interpretation of data, and the drafting and critical revision of the article.
Correspondence to: Maria Goretti Moreira Guimarães Penido, MD, PhD, Department of Pediatrics, Pediatric Nephrology Unit, School of Medicine, Federal University of Minas Gerais, Belo Horizonte, Belo Horizonte, CEP 30130100, Minas Gerais, Brazil. mariagorettipenido@yahoo.com.br
Telephone: +55-31-92991595 Fax: +55-31-32414466
Received: October 9, 2011
Revised: November 11, 2011
Accepted: February 10, 2012
Published online: April 6, 2012
Abstract

Idiopathic hypercalciuria (IH) is the leading metabolic risk factor for urolithiasis and affects all age groups without gender or race predominance. IH has a high morbidity with or without lithiasis and reduced bone mineral density (BMD), as described previously in pediatric patients as well as in adults. The pathogenesis of IH is complex and not completely understood, given that urinary excretion of calcium is the end result of an interplay between three organs (gut, bone and kidney), which is further orchestrated by hormones, such as 1,25 dihydroxyvitamin D, parathyroid hormone, calcitonin and fosfatonins (i.e., fibroblast growth-factor-23). Usually, a primary defect in one organ induces compensatory mechanisms in the remaining two organs, such as increased absorption of calcium in the gut secondary to a primary renal loss. Thus, IH is a systemic abnormality of calcium homeostasis with changes in cellular transport of this ion in intestines, kidneys and bones. Reduced BMD has been demonstrated in pediatric patients diagnosed with IH. However, the precise mechanisms of bone loss or failure of adequate bone mass gain are still unknown. The largest accumulation of bone mass occurs during childhood and adolescence, peaking at the end of the second decade of life. This accumulation should occur without interference to achieve the peak of optimal bone mass. Any interference may be a risk factor for the reduction of bone mass with increased risk of fractures in adulthood. This review will address the pathogenesis of IH and its consequence in bone mass.

Keywords: Bone mineral disease; Bone mineral density; Hypercalciuria; Children; Urine