Published online Feb 10, 2016. doi: 10.5317/wjog.v5.i1.110
Peer-review started: June 30, 2015
First decision: August 16, 2015
Revised: November 11, 2015
Accepted: December 13, 2015
Article in press: December 14, 2015
Published online: February 10, 2016
Processing time: 218 Days and 6 Hours
The literature on cervical embryonal rhabdomyosarcoma (RMS) is reviewed here to identify management guidelines for middle-aged women diagnosed with this rare type of gynecologic cancer. Specifically, the PubMed, Web of Science and Google Scholar databases, were searched to find published case series on cervical embryonal RMS reporting on four or more patients, of whom at least one was > 40-year-old. The χ2 test was used to assess heterogeneity. Five articles published between 1986 and 2013 were identified, reporting on a total of 47 patients, of whom 22 (46.8%) were older and 25 (53.2%) younger than 40-year-old. Although the two age groups did not differ significantly by stage of disease or radiotherapy treatment, the older age group received less chemotherapy (55% vs 90%, P = 0.008) and had more hysterectomy (86% vs 43%, P = 0.009). Follow-up data was missing for 18/47 (38.3%) patients. Among the 29 patients with follow-up data, survival was shorter in the older group, with 8/12 (67%) alive and 3 with disease at a median follow-up of 2.6 years, as compared with the younger group that had 15/17 (88%) alive and none with disease at a median follow-up of 3.5 years. The longest survivals among the older women were observed in those who received radiotherapy, including one case with a resected lung metastasis. A prospective multi-institutional collaboration and better follow-up are needed to determine the optimal management of cervical embryonal RMS. Long-term survival appears feasible if management is accompanied by chemotherapy and radiotherapy.
Core tip: The present review of adult cervical embryonal rhabdomyosarcoma case series summarizes 5 studies reporting on 47 female patients, 22 of whom were > 40-year-old. Women over 40 had worse disease-free survival but also received less chemotherapy administration. Although radiotherapy was not often used, the longest survival in the > 40 age group was observed among those who received radiotherapy, including a case with resected lung metastasis. The review argues for multimodality management in this rare disease.