Revised: January 18, 2013
Accepted: January 29, 2013
Published online: February 2, 2013
Processing time: 99 Days and 6.7 Hours
The term fibromatosis describes fibrotic tumor-like lesions of the skin which are seen in all age groups. They may be congenital or acquired and occur as single or multiple lesions. Classification of fibromatosis includes several clinical and pathologic variants. Progressive nodular fibrosis of the skin is a rare condition which has been scarcely reported in the literature and never in pediatric age. The clinical presentation is not specific showing asymptomatic, reddish-brown nodules. Histology shows abundance of spindle-shaped dermal fibroblasts. Here we describe an unusual pediatric case and discuss the diagnosis, which is possible only with histopathology, and the importance of differential diagnosis.
Core tip: Progressive nodular fibrosis of the skin is a rare condition characterized by asymptomatic, reddish-brown nodules resembling hypertrophic scars. Histology shows abundance of spindle-shaped dermal fibroblasts. It is mandatory to achieve a correct diagnosis.