Tandon YK, Rubin M, Kahlifa M, Doumit G, Naffaa L. Bilateral squamosal suture synostosis: A rare form of isolated craniosynostosis in Crouzon syndrome. World J Radiol 2014; 6(7): 507-510 [PMID: 25071892 DOI: 10.4329/wjr.v6.i7.507]
Corresponding Author of This Article
Yasmeen K Tandon, MD, Department of Radiology, Case Western Reserve University-Metro Health Medical Center, 2500 Metro Health Dr, Cleveland, OH 44109, United States. ytandon@neomed.edu
Research Domain of This Article
Radiology, Nuclear Medicine & Medical Imaging
Article-Type of This Article
Case Report
Open-Access Policy of This Article
This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
World J Radiol. Jul 28, 2014; 6(7): 507-510 Published online Jul 28, 2014. doi: 10.4329/wjr.v6.i7.507
Bilateral squamosal suture synostosis: A rare form of isolated craniosynostosis in Crouzon syndrome
Yasmeen K Tandon, Michael Rubin, Mohamed Kahlifa, Gaby Doumit, Lena Naffaa
Yasmeen K Tandon, Department of Radiology, Case Western Reserve University-Metro Health Medical Center, Cleveland, OH 44109, United States
Michael Rubin, Lena Naffaa, Department of Radiology, Akron Children’s Hospital, One Perkins Square, Akron, OH 44308, United States
Mohamed Kahlifa, Department of Medical Genetics, Akron Children’s Hospital, One Perkins Square, Akron, OH 44308, United States
Gaby Doumit, Department of Plastic Surgery, Cleveland Clinic, Cleveland, OH 44195, United States
Author contributions: Tandon YK, Rubin M, Kahlifa M, Doumit G and Naffaa L contributed equally to this work; Tandon YK, Naffaa L, Rubin M and Doumit G interpreted images in this study; Tandon YK, Rubin M, Kahlifa, Doumit G and Naffaa L and wrote the paper; Tandon YK, Rubin M, Kahlifa, Doumit G and Naffaa L gave final approval of the version to be published.
Correspondence to: Yasmeen K Tandon, MD, Department of Radiology, Case Western Reserve University-Metro Health Medical Center, 2500 Metro Health Dr, Cleveland, OH 44109, United States. ytandon@neomed.edu
Telephone: +1-216-7784016 Fax: +1- 216-7784375
Received: April 5, 2014 Revised: June 1, 2014 Accepted: June 14, 2014 Published online: July 28, 2014
Abstract
Craniosynostosis is a pathologic condition which is characterized by the premature fusion of cranial sutures. It may occur alone or in association with other anomalies making up various syndromes. Crouzon syndrome is the most common craniosynostosis syndrome. Bicoronal sutures fusion is most commonly involved in Crouzon syndrome. There have only been a handful of cases of squamosal suture synostosis described in the surgery literature with the few ones described in Crouzon syndrome associated with other types of craniosynostosis. To the best of our knowledge, we are presenting the first case of isolated bilateral squamosal suture synostosis in a patient with Crouzon syndrome in a radiology journal with emphasis on its radiological appearance.
Core tip: We report the unique case of isolated bilateral squamosal suture synostosis in a 13-mo old patient with Crouzon syndrome. Although bicoronal sutures are most commonly involved in patients with Crouzon syndrome, it is important to be familiar with this rare entity of craniosynostosis in order to prevent misdiagnosis or delayed surgical treatment.
