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©2011 Baishideng Publishing Group Co., Limited. All rights reserved.
World J Gastrointest Surg. Oct 27, 2011; 3(10): 156-158
Published online Oct 27, 2011. doi: 10.4240/wjgs.v3.i10.156
Published online Oct 27, 2011. doi: 10.4240/wjgs.v3.i10.156
A fatal case of Degos’ disease which presented with recurrent intestinal perforation
Mona Ahmadi, Sevil Agabalaey Rafi, Zhale Faham, Ramin Azhough, Samad Beheshty Rooy, Omid Rahmani, Department of General Surgery and Pathology, Imam Reza Hospital, Azadi Street, Tabriz 5156975389, Iran
Author contributions: All authors write this case report.
Correspondence to: Samad Beheshty Rooy, MD, Assistant Professor, Department of Surgery, Imam Reza Hospital, Azadi Street, Tabriz 5156975389, Iran. azhough@yahoo.com
Telephone: +98-411-3341317 Fax: +98-411-3341317
Received: April 2, 2011
Revised: September 21, 2011
Accepted: September 26, 2011
Published online: October 27, 2011
Revised: September 21, 2011
Accepted: September 26, 2011
Published online: October 27, 2011
Abstract
Degos’ disease, otherwise known as “malignant atrophic papulosis” is a rare vasculopathy with an unknown etiology characterized by typical cutaneous lesions. Involvement of the gastrointestinal (GI) tract is observed in approximately half of patients and small infarctions in the mucosa can cause perforation and resulting peritonitis, the leading cause of death. We present a fatal case of Degos’ disease with skin and GI involvement, manifesting as recurrent intestinal perforations and peritonitis, in a 15-year-old Iranian boy.