Case Report
Copyright ©The Author(s) 2016. Published by Baishideng Publishing Group Inc. All rights reserved.
World J Gastroenterol. Apr 7, 2016; 22(13): 3693-3700
Published online Apr 7, 2016. doi: 10.3748/wjg.v22.i13.3693
Pancreatic perivascular epithelioid cell tumor: A case report with clinicopathological features and a literature review
Hui Jiang, Na Ta, Xiao-Yi Huang, Ming-Hua Zhang, Jing-Jing Xu, Kai-Lian Zheng, Gang Jin, Jian-Ming Zheng
Hui Jiang, Na Ta, Xiao-Yi Huang, Ming-Hua Zhang, Jing-Jing Xu, Jian-Ming Zheng, Department of Pathology, Changhai Hospital, Second Military Medical University, Shanghai 200433, China
Kai-Lian Zheng, Gang Jin, Department of General Surgery, Changhai Hospital, Second Military Medical University, Shanghai 200433, China
Author contributions: Jiang H and Ta N contributed equally to this paper and wrote the paper; Jiang H diagnosed the case and interpreted the data; Ta N assisted with the literature retrieval and clinical data collection; Zheng KL and Jin G carried out the operation and patient follow-up; Huang XY, Zhang MH and Xu JJ helped perform the cytological and immunohistochemical diagnosis; all authors approved the final manuscript for publication.
Institutional review board statement: The study was reviewed and approved by the Shanghai Changhai Hospital Ethnic Committee.
Informed consent statement: The study was performed after obtaining the patient’s informed consent. The patient was treated according to the provisions of the Helsinki criteria.
Conflict-of-interest statement: We declare that we have no commercial or associative interest that represents a conflict of interest in connection with the work submitted.
Open-Access: This article is an open-access article which was selected by an in-house editor and fully peer-reviewed by external reviewers. It is distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/
Correspondence to: Jian-Ming Zheng, MD, Department of Pathology, Changhai Hospital, Second Military Medical University, Shanghai 200433, China. jmzheng1962@163.com
Telephone: +86-21-81873689 Fax: +86-21-81873689
Received: November 10, 2015
Peer-review started: November 12, 2015
First decision: December 11, 2015
Revised: December 27, 2015
Accepted: January 11, 2016
Article in press: January 11, 2016
Published online: April 7, 2016
Processing time: 139 Days and 5.7 Hours
Core Tip

Core tip: Perivascular epithelioid cell tumor (PEComa) of the pancreas is an unusual tumor deriving from mesenchyma. Via describing a rare case of pancreatic PEComa, we highlight the clinicopathological features of PEComa and conduct a literature review focusing on this tumor type so as to deepen the understanding of the subject. We also reviewed the biological behavior, prognosis, and therapeutic strategy of PEComa.