Published online Jan 28, 2021. doi: 10.3748/wjg.v27.i4.371
Peer-review started: November 23, 2020
First decision: December 8, 2020
Revised: December 16, 2020
Accepted: January 8, 2021
Article in press: January 8, 2021
Published online: January 28, 2021
Processing time: 62 Days and 20.2 Hours
Duplication of the extrahepatic bile duct (DCBD) is an extremely rare congenital anomaly of the biliary system. There are five types of DCBD according to the latest classification. Among them, Type V is characterized by single drainage of the extrahepatic bile ducts. Reports on DCBD Type V are scarce.
A 77-year-old woman presented with recurrent epigastric pain but without fever or chills. Computed tomography revealed a dilated common bile duct (CBD) that harboured multiple choledocholithiasis. Endoscopic retrograde cholangio-pancreatography (ERCP) was performed, and the stones were extracted using a Dormia basket. She was discharged without any complications; however, she visited the emergency department a day after she was discharged due to epigastric pain and fever. Laboratory findings were suggestive of cholestasis. After urgent ERCP for stone removal, magnetic resonance cholangiopancrea-tography was performed to evaluate remnant choledocholithiasis. Magnetic resonance cholangiopancreatography revealed a DCBD Type Va and remnant choledocholithiasis in the right CBD. Both CBDs were accessed, and the stones were cleared successfully during a subsequent ERCP.
In this article, we report an extremely rare case of DCBD manifesting as recurrent pyogenic cholangitis. This case highlights the importance of recognizing DCBD because stones in the unrecognized bile duct could make the patient’s prognosis critical.
Core Tip: Double common bile duct (DCBD) is an extremely rare congenital biliary tract anomaly. We present herein, a rare case of DCBD manifesting as a recurrent pyogenic cholangitis. It is substantial to establish complete stone clearance during endoscopic retrograde cholangiopancreatography because residual stone is a probable risk factor for recurrent cholangitis. However, DCBD, an extremely rare anomaly, can completely mask the presence of remnant bile duct stones for biliary endoscopists. In this case, recurrent cholangitis, which occurred immediately after bile duct stone clearance was a clue to recognize DCBD. Although this is a rare condition, our case highlights the importance of recognizing DCBD because stones in the unrecognized bile duct could make the patient’s prognosis critical.