Published online Dec 14, 2015. doi: 10.3748/wjg.v21.i46.13080
Peer-review started: July 20, 2015
First decision: August 26, 2015
Revised: September 7, 2015
Accepted: November 9, 2015
Article in press: November 9, 2015
Published online: December 14, 2015
Processing time: 142 Days and 20.7 Hours
AIM: To describe the ages at diagnosis and operation of biliary atresia (BA) and its incidence over a 15-year period in Taiwan.
METHODS: This was a population-based cohort study. BA cases were identified from the Taiwan National Health Insurance Research Database based on the International Classification of Diseases, Ninth Revision (ICD-9) code of BA 751.61 plus Kasai operation (ICD-9 procedure code 51.37) or liver transplantation (LT, ICD-9 procedure code 50.5). The patients’ characteristics including sex, age at diagnosis, age at receiving Kasai operation and age at receiving LT were compared among three birth cohorts: (1) 1997 to 2001; (2) 2002 to 2006; and (3) 2007 to 2011.
RESULTS: There were a total of 540 BA cases (275 females) with an incidence of 1.62 per 10000 live births. No seasonality of BA was noted. The mean ages at diagnosis of three cohorts were 57.9, 55.6 and 52.6 d. A linear regression model demonstrated a decreasing trend of the mean age at diagnosis (1.27 d per year). The proportion of BA cases that received the Kasai operation within 60 d of age increased from 76% to 81%. A total of 189 (35%) BA patients underwent LT. The mean age at LT was reduced from 3-year-old to 1-year-old. The rates of LT were 25.6% and 32.3% in patients who received the Kasai operation within 60 d or after 60 d of age, respectively. All patients who did not undergo a Kasai operation eventually required LT.
CONCLUSION: The ages at diagnosis and operation in BA cases have decreased over time. Kasai operation performed at younger age reduces the need for LT. The incidence of BA in Taiwan fluctuates, but without certain trend.
Core tip: Biliary atresia (BA) is an important liver disease of children. The age of diagnosis and operation for BA greatly affects its outcome. The incidence of BA varies among different studies and long-term trends are controversial. This study found the long-term incidence of BA in Taiwan has no increasing or decreasing trend. The age at diagnosis and operation of BA is continuously decreasing. The mean age at liver transplantation was reduced from 3-year-old to 1-year-old during the 15-year study period.