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World J Gastroenterol. Oct 14, 2006; 12(38): 6124-6127
Published online Oct 14, 2006. doi: 10.3748/wjg.v12.i38.6124
Published online Oct 14, 2006. doi: 10.3748/wjg.v12.i38.6124
Management of pseudomyxoma peritonei
Zhi-Bo Qu, Lian-Xin Liu, Department of General Surgery, First Clinical College of Harbin Medical University, Harbin 150001, Heilongjiang Province, China
Correspondence to: Lian-Xin Liu, Department of General Surgery, First Clinical College of Harbin Medical University, Harbin 150001, Heilongjiang Province, China. liulianxin@medmail.com.cn
Telephone: +86-451-53658828 Fax: +86-451-53670428
Received: December 21, 2005
Revised: December 28, 2005
Accepted: January 14, 2006
Published online: October 14, 2006
Revised: December 28, 2005
Accepted: January 14, 2006
Published online: October 14, 2006
Abstract
Pseudomyxoma peritonei (PMP) is a rare disease. It refers to a progressive disease process within the peritoneum which originates from the appendix or ovaries and is characterised by the production of copious amounts of mucinous fluid resulting in a “jelly belly”. If untreated the condition is fatal. The traditional approach to PMP is based on repeated surgical debulking procedures, often associated with intraperitoneal or systemic chemotherapy. The natural history of this disease has been drastically modified since the introduction of a new surgical approach defined as a peritonectomy procedure. This paper is to review the literature on this treatment strategy.
Keywords: Pseudomyxoma peritonei; Peritonectomy; Hyperthermic intraperitoneal chemotherapy; Sugarbaker procedures