Intimal sarcoma of the pulmonary artery with multiple lung metastases: Long-term survival case

Figure 1 Angio-computed tomography: Filling defect in pulmonary artery trunk measuring 58 mm × 32 mm × 44 mm, extending from the subvalvular area to the origin of the right pulmonary artery.

Figure 2 The patient was operated on for a suspected primary tumor of the pulmonary artery, resulting in with complete resection of the mass, whose pathological result was an intermediate-grade malignant tumor suggestive of Pulmonary artery intimal sarcoma. A: Macro: View of the pulmonary artery transversal section with infiltrating sarcoma on the lumen; B: High power of the tumor. Note the variable atypia 200 ×. Immunohistochemical stainings 100 ×; C: Smooth muscle actin: Focal tumor cell reaction 100 ×; D: Desmine: Negative 100 ×; E: CD31: Reaction of the endothelium surrounded by negative tumor cells 100 ×; F: Ki-67: Variable proliferation index in tumor cells 100 ×.

Figure 3 Positron emission tomography–computed tomography, three months later. A: Subpleural hypermetabolic nodular lesion in left upper lobe (SUV max 3.8) measuring 27 mm × 30 mm, suggestive of tumor activity; B and C: Computed tomography, a 38-mm nodule in right upper lobe and another 20-mm nodule in left upper lobe, compatible with metastasis.