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©2007 Baishideng Publishing Group Co.
World J Gastroenterol. Jun 28, 2007; 13(24): 3384-3387
Published online Jun 28, 2007. doi: 10.3748/wjg.v13.i24.3384
Published online Jun 28, 2007. doi: 10.3748/wjg.v13.i24.3384
Table 1 Review of the literature. Six cases with the coincidence of NET and GIST in Neurofibromatosis type 1 (NF1)
Patientage, sex | GISTLocation /Diameter | NETLocation + Histology/Diameter | Surgery | Follow up /outcome | Reference [no]/year of publication |
36, m | Jejunum 3, 5 cm | Papilla of vater n.i. 1, 2 cm | Duodeno-pancreatectomy | Two years/ well, no recurrence | Karatzas et al[10] 2000 |
60, m | Duodenojejunal n.i. | Pheochromocytoma (bilateral) n.i. | n.i. (Article in Italian) | n.i. | Rizzo et al[9] 2001 |
64, f | Duodenum, Jejeunum, Stomach Numerous: 0.5-2 cm | Papilla of vater Somatostatinoma n.i. | Local resection | n.i. | Usui et al[11] 2002 |
43, f | Jejunum 3, 5 cm | Duodenum neuroendocrine carcinoma 2, 7 cm | Duodeno-pancreatectomy | 54 mo/ well | Kramer et al[12] 2005 |
60, m | Small bowel numerous: cm | Pheochromocytoma (bilateral) | n.i. | n.i. | Lisewski et al[13] 2006 |
63, f | Ileum 6, 5 cm Jejunum (prerenal) 3 cm | Pheochromocytoma (metachron, bilateral) 5 cm, left adrenal gland right adrenal gland 3 cm | Adrenalectomy intestinal segment resection tumor resection jejunal resection | 48 mo/ well, no recurrence | as presented here |
Table 2 Time follow up of the presented case
Time | Tumor (size) | Localization | Treatment | |
0 | PCC (3 cm) GIST (6.5 cm) | Left adrenal gland ileo-terminal | Adrenalectomy segment resection | |
9 m | PCC (3 cm) GIST (3 cm) 7 x GIST (2 mm) | Right adrenal gland proximo-jejunal | Tumor-resection segment resection tumor resection | |
45 m | No tumor | Corticoid substitution |
- Citation: Kramer K, Hasel C, Aschoff AJ, Henne-Bruns D, Wuerl P. Multiple gastrointestinal stromal tumors and bilateral pheochromocytoma in neurofibromatosis. World J Gastroenterol 2007; 13(24): 3384-3387
- URL: https://www.wjgnet.com/1007-9327/full/v13/i24/3384.htm
- DOI: https://dx.doi.org/10.3748/wjg.v13.i24.3384