Retroperitoneal desmoplastic small round cell tumor: Pediatric patient treated with multimodal therapy

Figure 1 CT (A and B) shows a septated, very large (about 21. 8 cm × 16.7 cm), predominantly cystic, lobulated mass in the right upper quadrant between the liver and the right kidney.

Figure 2 Gross findings after resection show a hemorrhagic and necrotic solid mass with a focal fibrotic, granular cut surface.

Figure 3 Histopathological findings. Tumor cells consist of small round, hyperchromatic nucleus and scanty cytoplasm (Hematoxylin and eosin stain, × 400).

Figure 4 Immunohistochemical staining was positive for cytokeratin (A), vimentin (B), CD99 (C) and desmin (D) (× 400).