Cutaneous mucosa-associated lymphoid tissue lymphoma complicating Sjögren's syndrome: A case report and review of literature

Table 2 Literature reviews of 26 published cases or case series

Ref.	n	Age of SS diagnosis	Age of lymphoma onset	Sex	Sicca symptom	Risk factor	Anti-SSA/SSB	Lymphoma location	Stage (Ann Arbor)	Treatment	Prognosis
Xu et al[3]	4	NA	42	M	—	PGS	SSA/SSB	Parotid gland, thymus	IVA	Surgery	Improved
		NA	49	F	—	PGS, Monoclonal gammopathy, RF	SSA/SSB	Parotid gland, thymus	IVA	Surgery	Improved
		NA	49	F	—	Monoclonal gammopathy	SSA/SSB	Thymus	IVA	Surgery	Improved
		NA	38	F	—	RF	SSA/SSB	Thymus	IA	Surgery	Improved
Belfeki et al[6]	1	60	65	F	Dry eye, dry mouth	PGS, Monoclonal gammopathy, low C3, low C4	SSA	Breast	NA	NA	NA
Xian et al[7]	1	NA	45	F	NA	NA	NA	Lung	NA	Chemotherapy	Deceased
Arai et al[12]	1	NA	66	F	NA	RF	SSA	Thymus	NA	Surgery	Improved
Momoi et al[13]	1	52	58	F	NA	RF	SSA	Thymus	NA	Surgery, chemotherapy	Improved
Yoshida et al[14]	1	32	NA	F	NA	Monoclonal gammopathy	SSA	Thymus	NA	Surgery, chemotherapy	Improved
Hsu et al[15]	1	NA	54	F	Dry eye, dry mouth	NA	SSA	Mouth	IE	Surgery	Improved
De Vita et al[16]	1	41	46	F	Dry eye, dry mouth	PGS, cryoglobulins,RF, low C4	SSA/SSB	Parotid gland	IE	Belimumab, RTX	Improved
Kobayashi et al[17]	1	31	39	F	Dry eye	NA	SSA/SSB	Lung	I	GS	NA
Taylor et al[18]	1	NA	67	F	NA	NA	NA	Lung	NA	Surgery	NA
Baqir et al[19]	3	NA	74	F	Dry eye, dry mouth	NA	SSA/SSB	Lung	NA	NA	NA
		NA	48	F	Dry eye, dry mouth	NA	SSA/SSB	Lung	NA	NA	NA
		NA	53	F	Dry eye, dry mouth	NA	SSA/SSB	Lung	NA	NA	NA
Kluka et al[20]	1	33	53	F	Dry eye, dry mouth	Monoclonal gammopathy	SSA/SSB	Lung	I	HCQ, GS	NA
Keszler et al[21]	1	60	62	F	Dry eye, dry mouth	RF	—	Minor labial salivary gland	I	—	Improved
Watanabe et al[22]	1	29	49	F	Dry eye, dry mouth	NA	SSA/SSB	Lung	IV	Chemotherapy	Improved
De Vita et al[23]	1	45	51	F	Dry eye, dry mouth	PGS, cryoglobulins, RF, low C4	SSA/SSB	Parotid gland	IE	RTX	Improved
Covelli et al[25]	2	32	35	F	Dry eye, dry mouth	PGS, RF, low C4	SSA	Parotid gland	NA	RTX	NA
		42	44	F	Dry eye, dry mouth	Monoclonal gammopathy, RF	SSA/SSB	Lung	NA	GS, RTX	NA
Ornetti et al[26]	1	73	73	F	Dry eye, dry mouth	PGS	SSA	Parotid gland	NA	RTX, chemotherapy	Improved
Movahed et al[27]	1	36	41	F	Dry mouth	PGS	NA	Submandibular glands	III	—	Improved
Zenone et al[28]	2	55	56	F	Dry eye, dry mouth	PGS, cryoglobulins, RF	—	Parotid gland	NA	RTX, chemotherapy, radiotherapy	Progressive
		31	42	F	Dry eye, dry mouth	PGS, cryoglobulins, Monoclonal gammopathy	SSA/SSB	Parotid gland	NA	HCQ, RTX	Improved

PGS: Parotid gland swelling; RF: Rheumatoid factor; RTX: Rituximab; GS: Glucocorticoids; HCQ: Hydroxychloroquine; NA: Not available; “-”: Negative.