Pulmonary hypertension in hereditary haemorrhagic telangiectasia

Figure 1 Characteristic echocardiogram of a patient with pulmonary hypertension. A: Apical 4-chamber view showing dilatation of the right ventricle; B: Apical 4-chamber view with Doppler signal (continuous wave) showing an increased right ventricular- right atrial pressure gradient (4.4 m/s); C: Subcostal view showing dilatation of the inferior caval vein corresponding with an increased pressure in the right atrium; D: Parasternal short axis view showing flattening of the interventricular septum (D-sign) and dilatation of the right ventricle.