Copyright
©The Author(s) 2015.
World J Cardiol. May 26, 2015; 7(5): 230-237
Published online May 26, 2015. doi: 10.4330/wjc.v7.i5.230
Published online May 26, 2015. doi: 10.4330/wjc.v7.i5.230
Pulmonary arterial hypertension |
Idiopathic PAH |
Hereditable PAH |
BMPR2 |
ALK1, endoglin (with or without hereditary haemorrhagic telangiectasia), SMAD9, CAV1, KCNK3 |
Unknown |
Drug and toxin induced |
Associated with: |
Connective tissue diseases |
HIV infection |
Portal hypertension |
Congenital heart diseases |
Schistosomiasis |
Pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis |
Persistent pulmonary hypertension of the newborn |
Pulmonary hypertension due to left heart disease |
Left ventricular systolic dysfunction |
Left ventricular diastolic dysfunction |
Valvular disease |
Congenital/acquired left heart inflow/outflow tract obstruction and congenital cardiomyopathies |
Pulmonary hypertension due to lung diseases and/or hypoxia |
Chronic obstructive pulmonary disease |
Interstitial lung disease |
Other pulmonary diseases with mixed restrictive and obstructive pattern |
Sleep-disordered breathing |
Alveolar hypoventilation disorders |
Chronic exposure to high altitude |
Developmental abnormalities |
Chronic thromboembolic pulmonary hypertension |
PH with unclear and/or multifactorial mechanisms |
Haematological disorders: chronic haemolytic anaemia, myeloproliferative disorders, splenectomy |
Systemic disorders: sarcoidosis, pulmonary histiocytosis, lymphangioleiomyomatosis |
Metabolic disorders: glycogen storage disease, Gaucher disease, thyroid disorders |
Others: tumoural obstruction, fibrosing mediastinitis, chronic renal failure, segmental PH |
- Citation: Vorselaars VM, Velthuis S, Snijder RJ, Vos JA, Mager JJ, Post MC. Pulmonary hypertension in hereditary haemorrhagic telangiectasia. World J Cardiol 2015; 7(5): 230-237
- URL: https://www.wjgnet.com/1949-8462/full/v7/i5/230.htm
- DOI: https://dx.doi.org/10.4330/wjc.v7.i5.230