Redefining Budd-Chiari syndrome: A systematic review

Table 1 Epidemiology of classical Budd-Chiari syndrome and hepatic vena cava-Budd Chiari syndrome

Ref.	Country	Publication	Recruitment	n	Age	Gender		Location of obstruction (%)
		date	years		(median)	M (%)	F (%)	HV	IVC	Both
Janssen et al[27]	The Netherlands	2000	1984-1997	43	40	16 (37)	27 (63)
Perelló et al[40]	Spain	2002	1990-2000	21	361	5 (24)	16 (76)	17 (81)	0 (0)	4 (19)
Colaizzo et al[30]	Italy	2008	1997-2006	32	35	9 (28)	23 (72)
Darwish Murad et al[24]	Europe	2009	2003-2005	163	38	70 (43)	93 (57)	80 (49)	4 (2)	79 (48)
Xavier et al[31]	Brazil	2010	2000-2008	31	33	11 (35)	20 (65)
Sakr et al[22]	Egypt	2011	2009-2011	94	28.81	36 (38)	58 (62)	70 (74)	3 (3)	16 (17)
Deepak et al[29]	India	2011	2006-2009	20	36.6	14 (70)	6 (30)	17 (85)	1 (5)	2 (10)
Rautou et al[37]	France	2011	1995-2005	94	381	34 (36)	60 (64)	73 (78)		13 (14)
Raszeja-Wyszomirska et al[45]	Poland	2012	2004-2011	20	38	9 (45)	11 (55)
Westbrook et al[32]	United Kingdom	2012	1985-2008	66	36	27 (41)	39 (59)
D’Amico et al[34]	Italy	2013	2005-2011	31	46	14 (45)	17 (55)
Harmanci et al[42]	Turkey	2013	1989-2011	62	42.81	26 (42)	36 (58)	35 (56)	8 (14)	19 (30)
Nozari et al[47]	Iran	2013	1989-2012	55	291	22 (40)	33 (60)
Pavri et al[38]	United States	2014	2008-2013	47	42.4	16 (34)	31 (66)
Faraoun et al[25]	Algeria	2015	2008-2012	176	331	75 (43)	101 (57)	125 (71)	0 (0)	51 (29)
De et al[23]	India	2001	1992-1998	40	35.21	26 (65)	14 (35)	N/A	23 (72)	9 (28)
Xu et al[41]	China	2004	1983-2003	1360	33.21	833 (61)	527 (39)	2 (0)	1358 (100)2
Ebrahimi et al[46]	Iran	2011	2002-2008	21	421	11 (52)	10 (48)	6 (29)	12 (57)	3 (14)
Park et al[51]	South Korea	2012	1988-2008	67	47	34 (51)	33 (49)	5 (7)	56 (84)	6 (9)
Qi et al[35]	China	2013	1999-2011	169	38.31	66 (52)	61 (48)	53 (31)	20 (12)	96 (57)
Cheng et al[13]	China	2013	2010-2011	145	46	90 (6)	55 (38)	45 (31)	8 (6)	92 (63)
Qi et al[36]	China	2014	2012-2012	25	35.71	14 (56)	11 (44)	4 (16)	0 (0)	21 (84)
Zhou et al[26]	China	2014	2006-2010	338	41.71	209 (62)	129 (38)	45 (13)	8 (2)	285 (84)
Gao et al[49]	China	2015	2008-2012
R				98	363	62 (63)	36 (37)	31 (32)	26 (27)	41 (42)
NR				373	453	193 (52)	180 (48)	82 (22)	169 (45)	122 (33)

¹Mean values;

²No differentiation between IVC alone vs both IVC and hepatic vein;

³Provided median ages for the two groups separately. R: Recurrence of disease, NR: Non-recurrence of the disease; HV: Hepatic vein; IVC: Inferior vena cava; M: Male; F: Female; N/A: Not available.