Observational Study
Copyright ©The Author(s) 2023.
World J Hepatol. Jan 27, 2023; 15(1): 89-106
Published online Jan 27, 2023. doi: 10.4254/wjh.v15.i1.89
Table 1 International Classification of Diseases-10 code case definition for liver disease aetiology, stratified into hierarchical tiers based of clinical importance
Tier 1
Tier 2
Tier 3
DescriptorICD-10 codeDescriptorICD-10 code DescriptorICD-10 code
Autoimmune liver diseaseAutoimmune hepatitisK75.4Hepatitis not specifiedInflammatory liver disease unspecifiedK76.9MiscellaneousPeliosis hepatisK76.4
Primary biliary cholangitisK74.3Other specified inflammatory liver diseaseK75.8Other specified diseases of the liverK76.8
Granulomatous hepatitis not elsewhere specifiedK75.3Chronic hepatitis not elsewhere classifiedK73.0-K73.9Liver disorders in diseases classified elsewhereK77
Metabolic liver diseaseHaemochromatosisE83.11Congestive hepatopathyChronic passive congestion of the liverK76.1
Alpha 1 anti-trypsin deficiencyE88.01Central haemorrhagic necrosis of the liverK76.2
Wilson’s diseaseE83.01Hepatic veno-occlusive diseaseK76.5
HBVHepatitis B without DB18.1Toxic liver diseaseToxic liver diseaseK71
Hepatitis B with DB18.0
HCVHepatitis CB18.2
Alcohol-related liver diseaseAlcoholic liver diseaseK70-K70.9
Non-alcoholic fatty liver diseaseNon-alcoholic fatty liver diseaseK76.0