Cystic fibrosis associated liver disease in children

Table 6 Liver transplantation in cystic fibrosis liver disease - data from few published series

Ref.	Type	Number of pediatric recipients	Type of transplants	Males	Mean age at isolated liver transplantation (yr)	Lung function after Liver transplantation	5-year survival
Milkiewicz et al[45], 2002	Single center	9	Liver; Liver- lung -heart	Not available	15	Improved	Not available
Fridell et al[21], 2003	Single center	12	Liver	83%	10 ± 4.5	Improved or remained unchanged	75%
Molmenti et al[47], 2003	Single center	10	Liver	90%	9.7 (1.23–19)	Not available	60%
Mendizabal et al[44], 2011	Analysis of United Network for Organ Sharing database	148	Liver; Liver- lung (3.4%)	62%	11 ± 4.7	Not available	86%
Miguel et al[48], 2011	Single center	11	Liver	67%	12 (5.4–17)	Worsened or remained unchanged	> 85%
Dowman et al[49], 2012	Single center	19	Liver	Not available	11.8 (9.5–16.5)	Stable/improved initially, deteriorated > 5 years after transplant	> 60%