Vascular anomalies associated with hepatic shunting

Figure 4 Examples of congenital extrahepatic portosystemic shunts. A: Nineteen-month-old with congenital extrahepatic porto-systemic shunts (CEPSS) Type II. Connection (arrow) of portal vein to inferior vena cava (IVC). Reconstruction 3D rendering of a computed tomography scan; B and C: One year old with a history of heterotaxia, intestinal malrotation, pulmonary arteriovenous malformations and CEPSS Type II (orange arrow), portal vein (chevron) to IVC (star); D: Type II extrahepatic shunt superior mesenteric vein (chevron) and shunt (arrow) draining directly into the right atrium.