Copyright
©The Author(s) 2020.
World J Gastroenterol. Sep 28, 2020; 26(36): 5520-5526
Published online Sep 28, 2020. doi: 10.3748/wjg.v26.i36.5520
Published online Sep 28, 2020. doi: 10.3748/wjg.v26.i36.5520
Table 1 Summary of SMARCB1 deficient pancreatic undifferentiated rhabdoid carcinoma cases in the literature along with our case
Ref. | Age/gender | Size/pancreatic location | Histology | Treatment | Metastasis | Outcome | KRAS mutation | SMARCB1 (IHC) |
Agaimy et al[2] | 76/M | 5 cm/head | Rhabdoid | Surgery | NS | DOD in 1 mo | Wild type | Complete loss |
Agaimy et al[2] | 44/F | 6 cm/head | Rhabdoid, angiosarcoma-like | Surgery | NS | NS | Positive (pGly12Asp) | Complete loss |
Agaimy et al[2] | 72/M | 4 cm/head | Rhabdoid, pseudopapillary acantholytic gland-like spaces | Surgery | Liver, lymph nodes | DOD post-operatively | Wild type | Complete loss |
Agaimy et al[2] | 61/M | 5 cm/tail | Rhabdoid, prominent neutrophils and focal glandular formation | Surgery | Intra-abdominal, stomach | NS | Wild type | Complete loss |
Sano et al[3] | 68/F | 10 cm/body, tail | Rhabdoid | Palliative | Liver, kidneys, lungs, right adrenal gland, omentum, peritoneum | DOD in 2 wk | NS | Complete loss |
Ohike et al[4] | 35/F | 6 cm/head | Rhabdoid, solid/diffuse | Chemo | Liver | DOD in 7 mo | Wild type | Complete loss |
Tahara et al[5] | 67/F | 1.9 cm/body | Rhabdoid, solid/diffuse | Chemo | Liver, lung, bone, tongue, right thigh | DOD in half year | Wild type | Complete loss |
Lehrke et al[6] | NS | NS | Rhabdoid | NS | NS | NS | NS | Complete loss |
Our case | 59/F | 3.1 cm/head | Rhabdoid, solid pseudopapillary-like | Surgery | Liver | DOD in 7 mo | Wild type | Complete loss |
- Citation: Hua Y, Soni P, Larsen D, Zreik R, Leng B, Rampisela D. SMARCB1/INI1-deficient pancreatic undifferentiated rhabdoid carcinoma mimicking solid pseudopapillary neoplasm: A case report and review of the literature. World J Gastroenterol 2020; 26(36): 5520-5526
- URL: https://www.wjgnet.com/1007-9327/full/v26/i36/5520.htm
- DOI: https://dx.doi.org/10.3748/wjg.v26.i36.5520