Risk of malignancy in Caroli disease and syndrome: A systematic review

Table 4 Surgical treatment, tumor characteristics and survival

Ref.	Surgery for all patients (LR vs OLT)1	TNM	1-yr survival cancer patients	Recurrence
Ammori et al[27]	50% vs 50%	No data	33%	0%
De Kerckhove et al[19]	0% vs 100%	No data	66%	33%
Kassahun et al[21]	87% vs 0%	No data	0%	33%
Habib et al[17]	0% vs 100%	No data	0%	No data
Bockhorn et al[30]	83% vs 17%	n = 1 pT1, n = 1 pT2	66%	0%
Millwala et al[5]	0% vs 100%	No data	0%	No data
Ulrich et al[3]	90% vs 10%	No data	0%	No data
Hori et al[24]	0% vs 100%	No data	No data	No data
Lendoire et al[13]	91.6% vs 0%	No data	100%	No data
Mabrut et al[20]	75% vs 18.9%	n = 6 R0, n = 1 peritoneal seeding	33%	50%
Moslim et al[12]	22% vs 78%	No data	0%	33%, 66% tumor progression
Fahrner et al[25]	90% vs 10%	n = 1 pT1N1, n = 2 pT2, n = 1 pT3	100%	75%

¹Besides liver resection and orthotopic liver transplantation, other surgical interventions performed, so that the sum of the percentages does not equal 100%. LR: Liver resection; OLT: Orthotopic liver transplantation; TNM: Tumor-nodes-metastases.