Risk of malignancy in Caroli disease and syndrome: A systematic review

Table 3 Patient demographics, duration of disease and tumor identification

Ref.	Age (yr)	Female sex (%)	Duration of disease	Tumor identification
Ammori et al[27]	35	75	No data	No data
De Kerckhove et al[19]	39.7	52	No data	No data
Kassahun et al[21]	51.5	55	< 1 yr 51%, 1-5 yr 13%, > 5 yr 35%	No data
Habib et al[17]	26	50	No data	No data
Bockhorn et al[30]	39	42	No data	67% incidental finding
Millwala et al[5]	35	55	No data	No data
Ulrich et al[3]	49	55	< 1 yr 55%, > 5 yr 2.5%	100% incidental finding
Hori et al[24]	23.74	No data	6.4 yr	100% puncture of nodule prior surgery
Lendoire et al[13]	48.7	70	2.6 yr	100% incidental finding
Mabrut et al[20]	55.7	43	7 mo	No data
Moslim et al[12]	40	22	No data	100% incidental finding
Fahrner et al[25]	56	74	No data	75% incidental finding 25% suspicious nodules in diagnostics