Risk of malignancy in Caroli disease and syndrome: A systematic review

Table 1 Literature search results and analyzed manuscripts

Ref.	Country	Year of publication	Type of study	n of reported patients	n of cancer (%)
Ammori et al[27]	United Kingdom	2002	Single-center, retrospective	8	3 (37.5)
De Kerckhove et al[19]	Belgium	2005	ELTR registry, retrospective	113	3 (2.7)
Kassahun et al[21]	Germany	2005	Single-center, retrospective	33	3 (9)
Habib et al[17]	United States	2006	Single-center, retrospective	33	1 (3)
Bockhorn et al[30]	Germany	2006	Single-center, retrospective	12	3 (25)
Millwala et al[5]	United States	2008	UNOS registry, retrospective	104	3 (2.9)
Ulrich et al[3]	Germany	2008	Single-center, retrospective	44	4 (9)
Hori et al[24]	Japan	2010	Single-center, retrospective	5	1 (20)
Lendoire et al[13]	Argentina	2011	Multicenter, retrospective	24	1 (4.2)
Mabrut et al[20]	France	2013	Multicenter, retrospective	155	8 (5)
Moslim et al[12]	United States	2015	Single-center, retrospective	9	3 (33.3)
Fahrner et al[25]	Germany	2018	Single-center, retrospective	21	4 (19)

ELTR: European Liver Transplant Registry; UNOS: United Network of Organ Sharing.