First case of IgG4-related sclerosing cholangitis associated with autoimmune hemolytic anemia

Table 1 Laboratory data

	Initial presentation	At time of cholangitis	After steroid treatment
White blood cells (× 109/L)	5.8	19.5	7.2
Red blood cells (× 1012/L)	3.97	0.94	3.91
Hemoglobin (g/L)	129	41	127
Hematocrit	38%	11.5%	39.2%
Platelets (× 109/L)	223	319	212
Reticulocytes	19‰	320‰	15‰
Haptoglobin (mg/L)	-	100	-
Total bilirubin (μmol/L)	7	728	9
Direct bilirubin (μmol/L)	3	616	3
Aspartate aminotransferase (IU/L)	63	144	16
Alanine aminotransferase (IU/L)	149	110	12
Alkaline phosphatase (IU/L)	1056	1151	131
γ-Glutamyl transpeptidase (IU/L)	784	302	16
Lactate dehydrogenase (IU/L)	205	1397	184
C-reactive protein (nmol/L)	32	137	< 10
IgG (g/L) (NR 8.7-17.0)	18	16.6	11.4
IgG4 (g/L) (NR 0.048-1.05)	2.3	-	1.0
Carbohydrate antigen 19-9 (U/mL)	15.2	94.2	22.8

NR: Normal range.